Resultado da estimulação elétrica intramuscular como tratamento adjuvante da síndrome do homem rígido
relato de caso
Palavras-chave:
“SÍNDROME DO HOMEM RÍGIDO”, ANTI-GAD56, ESPASMO MUSCULAR: TIMOMA, ESTIMULAÇÃO ELÉTRICA INTRAMUSCULAR, ELETROACUPUNTURAResumo
A “Síndrome da Pessoa Rígida” é uma doença rara do sistema nervoso central, mais prevalente em mulheres, entre 30 e 60 anos, que cursa com contratura espástica intermitente, dolorosa, da musculatura de tronco e membros. Considera-se a origem autoimune, pela frequente associação à outras doenças autoimunes, como diabetes tipo I, e pela presença de anticorpos anti-GAD65 (against 65-kDa glutamicaciddecarboxylase) na maioria desses indivíduos. Apresentamos relato de caso de paciente masculino jovem, com quadro de contratura muscular espástica generalizada, precedido por timoma, com repercussão motora e ventilatória progressivas, tratado com farmacoterapia e estimulação elétrica intramuscular/eletroacupuntura.
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