Síndrome de ortodeoxia-platipneia associada a comunicação interatrial: um relato de caso

Eduardo  Poitevin Cruz; Marcelo  Vitola Dreckmann; Felipe  Barbosa Amaral; Marcelo José  Linhares; Júlio Cesar  Schulz; Fabricio Martins  Zucco; Giulliano Gardenghi

doi:10.63162/v66n67e25526

Authors

Eduardo Poitevin Cruz Residente em Cardiologia, Clínica CARDIOPRIME Hospital Santa Catarina, Blumenau, SC, Brasil Autor https://orcid.org/0009-0002-3611-4424
Marcelo Vitola Dreckmann Residente em Cardiologia, Clínica CARDIOPRIME Hospital Santa Catarina, Blumenau, SC, Brasil Autor https://orcid.org/0009-0004-4244-9444
Felipe Barbosa Amaral Cardiologista intervencionista, CARDIOPRIME, Hospital Santa Catarina, Blumenau, SC, Brasil Autor https://orcid.org/0000-0003-3208-7553
Marcelo José Linhares Cardiologista, CARDIOPRIME, Hospital Santa Catarina, Blumenau, SC, Brasil Autor https://orcid.org/0009-0006-0715-6210
Júlio Cesar Schulz Cardiologista intervencionista, CARDIOPRIME, Hospital Santa Catarina, Blumenau, SC, Brasil Autor https://orcid.org/0009-0009-2141-2227
Fabricio Martins Zucco Cirurgião Vascular e Endovascular, Hospital Santa Catarina, Blumenau, SC, Brasil Autor https://orcid.org/0000-0003-4804-0696
Giulliano Gardenghi Coordenador científico / Hospital ENCORE, Aparecida de Goiânia – Goiás – Brasil Autor https://orcid.org/0000-0002-8763-561X

DOI:

https://doi.org/10.63162/v66n67e25526

Keywords:

Dyspnea, Interatrial communication, Hypoxia, Cardiology, Rare Syndromes

Abstract

Orthodeoxia-platypnea syndrome (POS) is a rare clinical condition, with few reports in the literature. Characterized
by the presence of a pulmonary arteriovenous shunt (arteriovenous malformation and hepatopulmonary
syndrome) or intracardiac right-to-left shunt (patent foramen ovale and/or related interatrial septal defects). Atrial
septal defect (ASD) is the most prevalent cause of POS, representing around 87% of cases. The treatment of this
syndrome varies according to its etiology. In this report, a POS situation associated with the presence of an ASD is
presented, and the diagnostic strategy and approach used to treat this condition are discussed.

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