Complete atrioventricular block in a patient with Turner’s syndrome

Abstract

Turner’s syndrome is associated with a wide variety of anatomical and physiological anomalies, especially alterations in the cardiovascular system. Bicuspid aortic valve, coarctation and dilatation of the aorta are the most common. Although conduction disorders are rare, they may occur. The aim of this paper is to report a case of complete atrioventricular block in a patient with Turner’s syndrome. 51-year-old, female, white, single, born and residing in Goiânia and carrier of Turner’s syndrome was seen complaining of dyspnea during moderate effort, palpitation, dizziness and malaise. The patient had had previous diagnoses of valvular dysfunction (mild mitral and tricuspid regurgitation and aortic lesion, with moderate stenosis and mild regurgitation) plus bicuspid aortic valve. She kept an irregular cardiac monitoring. In medical evaluation, atrioventricular block was evident. Aiming at reduction of morbidity and mortality among patients with Turner’s syndrome, disturbances in atrioventricular conduction, although rare, should not be forgotten or confused with other cardiac abnormalities most commonly found in this group.